Abstract
Introduction: We report a case of spontaneous rupture of a renal angiomyolipoma during pregnancy
which is rare and occasionally fatal. A 30-year-old woman was referred at 38 weeks of gestation with left flank
pain, preeclampsia and anemia. The gynecologists performed an emergency cesarean section for fetal distress
and found moderate retroperitoneal hematoma during the operation. Conservative management was
recommended for the retroperitoneal hematoma. However, after delivery, her hemodynamic status continued
to detoriorate despite blood transfusions. Further work-up with abdominal computed tomography reveled a
large left renal angiomyolipoma with spontaneous rupture. Left total nephrectomy was performed without
complications by transperitoneal approach because of tumor localization and unstable hemodynamic
condition of the patient