Abstract

Angiomyolipomas are one of the most common benign tumors of the kidney and can affect vascular, smooth muscle and adipose tissue. Cystic angiomyolipomas have recently been described as a variant of the classic angiomyolipoma, and fewer than 20 cases have been reported in the English literature. A review of the English literature was conducted using the Pubmed/Medline database concerning cystic angiomyolipoma of the kidney. Cystic angiomyolipomas, or angiomyolipomas with epithelial cysts, are extremely rare, and fewer than 20 cases have been reported in the literature according to the Pubmed/Medline database. Herein, we report a case of cystic angiomyolipoma of the kidney in a 62-year-old male patient. The angiomyolipoma presented components of smooth muscle tissue, blood vessels and mature adipose tissue accompanying the epithelial cyst, which was lined by cuboidal cells. To the best of our knowledge, this is the first case report of cystic angiomyolipoma in Turkey. Cystic angiomyolipoma of the kidney is a very rare variant of classic angiomyolipoma with distinct pathological features.