Abstract

We report on a 2-year-old boy who was referred to our clinic with recurrent urinary tract infections, neurogenic bladder dysfunction and duplicated urethra. The child was unable to void spontaneously, and a suprapubic catheter had been placed. We performed an internal urethrotomy on his patent urethra, but the procedure did not successfully restore spontaneous voiding. After the surgery, we evaluated the child for the presence of congenital syndromes, especially the MURCS (Mullerian-Renal-Cervical Spine) association. Six months later, the patient underwent a left orchiopexy procedure. There was no evidence of the right testis. This case shows that the male variant of the MURCS association may accompany miscellaneous urogenital anomalies such as renal agenesis, cross renal ectopy, vesicoureteral reflux, neurogenic bladder dysfunction, posterior urethral valve, duplicated urethra, bilateral/unilateral undescended testes or vanishing testis.