Abstract
Myxomas are uncommon soft-tissue neoplasms, which are extremely rare in the kidney. In the present case, a right nephrectomy was performed because of suspected presence of a malignant renal tumor. In the macroscopic examination, the kidney contained a well-circumscribed, yellowish, and gelatinous tumor. The tumor was measured 6 cm in diameter. It was composed of fibroblast-like, slender spindle cells with myxoid stroma. With these histopathological findings, the case was diagnosed as renal myxoma. The case was discussed in the light of literature.